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Pulmonology
Congenital Pulmonary Disorders
Congenital and inherited lung disease for the FRACP written exam: adult diagnosis of cystic fibrosis by sweat chloride bands and CFTR genotype, CFTR-related disorder and CFSPID; CFTR modulators by genotype (ivacaftor, lumacaftor, tezacaftor, elexacaftor-tezaca…
11 lessons and 30 exam-style questions, written for the RACP Divisional Written Exam
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1Congenital Pulmonary Disorders
- Cystic Fibrosis in Adults: Genotype, Sweat Chloride and Diagnosis
- Cystic Fibrosis: CFTR Modulators by Genotype, Interactions and Liver Monitoring
- Cystic Fibrosis: Airway Clearance, Pseudomonas and Exacerbations
- Cystic Fibrosis: Burkholderia, NTM, Haemoptysis, Pneumothorax and Transplant
- Cystic Fibrosis: Diabetes, Gut, Liver, Bone, Cancer Screening and Fertility
- Alpha-1 Antitrypsin Deficiency: Who to Test, Levels, Genotypes and Risk
- Alpha-1 Antitrypsin Deficiency: Smoking, Augmentation, Lung Volume Reduction and Transplant
- Primary Ciliary Dyskinesia: When to Suspect It and How to Confirm It
- Primary Ciliary Dyskinesia: Airway Management, Ears and Fertility
- Congenital Lung Malformations Presenting in Adults
- Exam Pearls